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- Title
Linear IgA bullous dermatosis of childhood: Retrospective single‐center cohort.
- Authors
Wang, Katherine L.; Lehman, Julia S.; Davis, Dawn M. R.
- Abstract
Linear IgA bullous dermatosis (LABD) is a rare autoimmune blistering disorder impacting children and adults. In this single‐center retrospective chart review of pediatric patients with LABD at a large tertiary referral center, we report the unifying and unique clinical features of 10 pediatric patients. Patients typically presented with the "cluster of jewels" sign (n = 6; 60%), mucous membrane involvement (n = 5; 50%) and had a mean disease duration of 38 months; six patients (60%) required inpatient admission for management of their skin disease, including all five patients who had mucous membrane involvement. Our findings suggest that pediatric LABD may be a disease with high morbidity and may be associated with severe complications when mucous membranes are involved.
- Subjects
MUCOUS membranes; BULLOUS pemphigoid; CHILD patients; AUTOIMMUNE diseases; DISEASE management; DISEASE duration
- Publication
Pediatric Dermatology, 2024, Vol 41, Issue 3, p461
- ISSN
0736-8046
- Publication type
Article
- DOI
10.1111/pde.15567