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- Title
Cecal Volvulus in a Child with CHARGE Syndrome.
- Authors
Hong-Shiee Lai; Chi-Yen Feng
- Abstract
Cecal volvulus occurring in a child with CHARGE syndrome is presented. This boy was known to have CHARGE syndrome with multiple congenital anomalies, including coloboma, ventricular septal defect, choanal atresia, growth and mental retardation, bilateral cryptorchidism, dysplasia of the right ear, cleft lip, and hydrocephalus. Nissen's fundoplication had been previously performed for severe hiatal hernia and gastroesophageal regurgitation at the age of 1 year. Cecal volvulus occurred with a 540-degree clockwise rotation of terminal ileum to the right transverse colon and a displacement of the rotated loop to the right upper quadrant of the abdomen when he was 10 years old. Right hemicolectomy with divided ileo- and colostomy was performed. A second staged ileocolostomy was performed uneventfully 3 months later. The midline structural defects with nonfixation of the cecum and ascending colon, chronic constipation, and previous abdominal surgery might have been the predisposing factors.
- Subjects
VOLVULUS; SYNDROMES in children; FUNDOPLICATION; RIGHT hemicolectomy; GENETIC disorders
- Publication
American Surgeon, 2006, Vol 72, Issue 4, p356
- ISSN
0003-1348
- Publication type
Article
- DOI
10.1177/000313480607200417