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- Title
Generalized atrophic benign epidermolysis bullosa – poor prognosis associated with chronic renal failure.
- Authors
Woo, H. J.; Lee, J. H.; Kim, S. C.; Kim, C. W.; Kim, T. Y.
- Abstract
Generalized atrophic benign epidermolysis bullosa (GABEB) is an autosomal recessive form of junctional epidermolysis bullosa, with milder clinical features than the Herlitz subtype. A 25-year-old man presented with the clinical and histological findings of GABEB. At the initial visit, laboratory tests revealed that he also had chronic renal failure (CRF). Usually, GABEB has a good prognosis. However, in this case, the patient had CRF as an associated complication. He died of an intracranial haemorrhage combined with sepsis after 3 weeks of hospitalization. This case suggests that renal complications can occur in this relatively mild form of epidermolysis bullosa, and may contribute to morbidity and premature mortality.
- Subjects
EPIDERMOLYSIS bullosa; CUTANEOUS manifestations of general diseases; CHRONIC kidney failure; DIAGNOSIS
- Publication
Clinical & Experimental Dermatology, 2000, Vol 25, Issue 3, p212
- ISSN
0307-6938
- Publication type
Article
- DOI
10.1046/j.1365-2230.2000.00617.x