We found a match
Your institution may have rights to this item. Sign in to continue.
- Title
What Is Hemidystonia?
- Authors
Vizcarra, Joaquin A.; Jinnah, Hyder A.
- Abstract
Background: Hemidystonia is defined as dystonia restricted to one side of the body. It is traditionally believed to result from a lesion in the contralateral hemisphere. Objectives: To describe a series of hemidystonia patients without lesions on brain imaging. Methods: We searched for individuals with potential hemidystonia who were included in the Dystonia Coalition or Movement Disorder Society Genetic mutation database (MDSgene), and conducted a systematic review. Results: We found 10 individuals classified as hemidystonia or with homolateral limb dystonia among 3696 cases enrolled by the Dystonia Coalition, 9 cases in MDSgene, and one idiopathic case in the literature. None had evidence of a brain lesion. Body distributions used to define hemidystonia varied considerably and were not always restricted to one side of the body. Conclusions: Hemidystonia may be idiopathic or genetic, without any obvious brain lesion. The varied use of the term suggests the need for more specific clinical criteria to define "half the body."
- Subjects
GENETIC disorders; BRAIN damage; GENETIC databases; DYSTONIA; GENETIC mutation; MOVEMENT disorders
- Publication
Movement Disorders Clinical Practice, 2023, Vol 10, Issue 3, p477
- ISSN
2330-1619
- Publication type
Article
- DOI
10.1002/mdc3.13659