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- Title
Peutz-Jeghers Syndrome.
- Authors
McGarrity, Thomas J.; Kulin, Howard E.; Zaino, Richard J.
- Abstract
Peutz-Jeghers syndrome (PJS) is an unusual polyposis syndrome that has enjoyed a rich and somewhat confusing history. Mucocutaneous pigmentation and diffuse gastrointestinal hamartomas are the hallmark features of this autosomal dominant inherited condition. Peutz-Jeghers syndrome is now also recognized as a cancer predisposition syndrome. In this review, we highlight the historical aspects of PJS polyposis with special emphasis on its extraintestinal manifestations, particularly genital tract tumors. A PJS management scheme for clinicians is included.
- Subjects
PEUTZ-Jeghers syndrome; INTESTINAL polyps; PIGMENTATION disorders; GASTROINTESTINAL diseases; TUMORS
- Publication
American Journal of Gastroenterology (Springer Nature), 2000, Vol 95, Issue 3, p596
- ISSN
0002-9270
- Publication type
Article
- DOI
10.1111/j.1572-0241.2000.01831.x