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- Title
Shone's syndrome diagnosed with echocardiography and confirmed at pathology.
- Authors
Popescu, Bogdan A.; Jurcut, Ruxandra; Serban, Marinela; Parascan, Liliana; Ginghina, Carmen
- Abstract
The Shone's complex, defined by four cardiovascular defects such as a supravalvular mitral membrane, valvular mitral stenosis by a parachute mitral valve, subaortic stenosis, and aortic coarctation, is a rare entity, which occurs most frequently in its incomplete form. We report the case of a 19-year-old female patient who presented at the emergency room for progressively worsening dyspnoea, orthopnoea, fever, and productive cough, due to bronchopneumonia. Echocardiography revealed the co-existence of aortic coarctation with bicuspid aortic valves, mitral supravalvular ring, and dysplastic mitral valves producing severe mitral stenosis and severe pulmonary hypertension. Although wide spectrum antibiotics were administered from the first day of hospitalization, the patient developed severe sepsis and died. The components of the Shone's complex diagnosed by echocardiography were confirmed at pathology.
- Subjects
MITRAL stenosis; ECHOCARDIOGRAPHY; AORTIC coarctation; PULMONARY hypertension treatment; ANTIBIOTICS
- Publication
European Journal of Echocardiography, 2008, Vol 9, Issue 6, p865
- ISSN
1525-2167
- Publication type
Article
- DOI
10.1093/ejechocard/jen200