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- Title
Acute liver failure in young children with systemic-onset juvenile idiopathic arthritis without macrophage activation syndrome: Report of two cases.
- Authors
Hiejima, Eitaro; Komatsu, Haruki; Takeda, Yoshitake; Sogo, Tsuyoshi; Inui, Ayano; Okafuji, Ikuo; Nishikomori, Ryuta; Nakahata, Tatsutoshi; Fujisawa, Tomoo
- Abstract
Acute liver failure (ALF) with macrophage activation syndrome (MAS) is well known as a complication of systemic-onset juvenile idiopathic arthritis (S-JIA). However, liver failure without overt MAS is rare in S-JIA. We encountered two Japanese children with S-JIA in whom ALF developed during the remission of clinical manifestations. ALF without MAS was improved with plasma exchange and cyclosporine A combined with pulse methylprednisolone.
- Subjects
LIVER failure; BLOOD plasma; BLOOD transfusion; IMMUNOSUPPRESSIVE agents; CYCLOSPORINE
- Publication
Journal of Paediatrics & Child Health, 2012, Vol 48, Issue 3, pE122
- ISSN
1034-4810
- Publication type
Article
- DOI
10.1111/j.1440-1754.2011.02213.x