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- Title
Necrotic Uveal Melanoma Mimics Orbital Cellulitis: A Review.
- Authors
Abdel-Aty, Ahmad; Linderman, Wendy L.; Kombo, Ninani; Sinard, John; Pointdujour-Lim, Renelle
- Abstract
Background: Uveal melanoma is the most common primary intraocular malignancy in adults, often resulting in painless vision loss. We report a case of necrotic uveal melanoma presenting with orbital inflammation mimicking orbital cellulitis and present a comprehensive review of the literature and tabulation of reported cases. Summary: Our review found 44 published reports of spontaneously necrotic uveal melanoma involving 55 patients. Of these reports, 26 patients (47%) presented with orbital cellulitis. Presenting symptoms of necrotic uveal melanoma with orbital cellulitis included proptosis (82.8%), pain (80.7%), vision loss (61.5%), and restricted extraocular movements (46.2%). Key Messages: Uveal melanoma can rarely mimic orbital cellulitis. Autoinfarction and tumor necrosis causes secondary orbital inflammation. Intraocular malignancy must remain in the differential for patients with orbital inflammation and vision loss.
- Publication
Ocular Oncology & Pathology, 2022, Vol 8, Issue 1, p1
- ISSN
2296-4681
- Publication type
Article
- DOI
10.1159/000515558