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- Title
Mauriac Syndrome: Case Report and Review of the Literature.
- Authors
Topaloğlu, Ömercan; Sezer, Sibel Demiral; Demir, Bilgin; Akarken, Derya
- Abstract
This is a case report of a young male with poorly controlled type 1 diabetes mellitus who presented with the clinical features of diabetic ketoacidosis. Once the patient was stabilized, he was examined for hepatomegaly and elevated liver enzymes. Along with the other clinical features, the patient was diagnosed as a case of Mauriac Syndrome. Mauriac Syndrome, initially described by Mauriac in 1930, is one of the causes of hepatomegaly and elevated liver enzymes in poorly controlled diabetic patients. However, hepatomegaly, growth retardation and other clinical features of the syndrome have been found to be reversible with optimization of insulin therapy. In patients with poorly controlled diabetes, Type 1 diabetic patients must be closely observed for sexual maturation and growth. After optimal therapy has been given, close follow-up is essential to observe the regression of clinical features.
- Subjects
INSULIN therapy; ADOLESCENCE; PEOPLE with diabetes; HUMAN growth; TYPE 1 diabetes; LIVER function tests; MEDICAL referrals; LITERATURE reviews; GLYCOGENOLYSIS; HEPATOMEGALY; GLYCEMIC control; DISEASE complications
- Publication
Turkish Journal of Endocrinology & Metabolism, 2017, Vol 21, Issue 4, p131
- ISSN
1301-2193
- Publication type
Article
- DOI
10.25179/tjem.2017-56496