Fetal valproate syndrome, which is seen in children of epileptic mothers who have taken sodium valproate during their pregnancy, is characterized by typical facial appearance, major and minor malformations and neurodevelopmental delay. A case with facial features including epicanthal folds, depressed nasal bridge, hypertelorism, retrognathia, low set ears and peripheral pulmonary artery stenosis, patent ductus arteriosus and overlapping toes is presented for reminding this syndrome.