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Azithromycin in Patients With Cystic Fibrosis Chronically Infected With Pseudomonas aeruginosa: A Randomized Controlled Trial.
- Published in:
- JAMA: Journal of the American Medical Association, 2003, v. 290, n. 13, p. 1749, doi. 10.1001/jama.290.13.1749
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- Publication type:
- Article
Bronchoalveolar lavage fluid cytokine profiles in neuroendocrine cell hyperplasia of infancy and follicular bronchiolitis.
- Published in:
- 2013
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- Publication type:
- journal article
Pulmonary exacerbations and clinical outcomes in a longitudinal cohort of infants and preschool children with cystic fibrosis.
- Published in:
- 2017
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- Publication type:
- journal article
Gene modifiers in cystic fibrosis.
- Published in:
- 2008
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- Publication type:
- journal article
Vitamin E Deficiency Neuropathy in Children with Fat Malabsorption Studies in Cystic Fibrosis and Chronic Cholestasis<sup>a</sup>.
- Published in:
- Annals of the New York Academy of Sciences, 1989, v. 570, n. 1, p. 156, doi. 10.1111/j.1749-6632.1989.tb14916.x
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- Publication type:
- Article
Sputum induction improves detection of pathogens in children with cystic fibrosis.
- Published in:
- Pediatric Pulmonology, 2015, v. 50, n. 7, p. 638, doi. 10.1002/ppul.23150
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- Publication type:
- Article
Anti-PcrV antibody in cystic fibrosis: A novel approach targeting Pseudomonas aeruginosa airway infection.
- Published in:
- Pediatric Pulmonology, 2014, v. 49, n. 7, p. 650, doi. 10.1002/ppul.22890
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- Publication type:
- Article
Abnormal infant pulmonary function in young children with neuroendocrine cell hyperplasia of infancy.
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- Pediatric Pulmonology, 2013, v. 48, n. 10, p. 1008, doi. 10.1002/ppul.22718
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- Publication type:
- Article
Urinary desmosine: A biomarker of structural lung injury during CF pulmonary exacerbation.
- Published in:
- Pediatric Pulmonology, 2012, v. 47, n. 9, p. 856, doi. 10.1002/ppul.22525
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- Publication type:
- Article
Pulmonary exacerbations in cystic fibrosis with negative bacterial cultures.
- Published in:
- Pediatric Pulmonology, 2010, v. 45, n. 6, p. 569, doi. 10.1002/ppul.21221
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- Publication type:
- Article
Lessons learned from a randomized trial of airway secretion clearance techniques in cystic fibrosis.
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- Pediatric Pulmonology, 2010, v. 45, n. 3, p. 291, doi. 10.1002/ppul.21179
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- Publication type:
- Article
Relationship between antimicrobial proteins and airway inflammation and infection in cystic fibrosis.
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- Pediatric Pulmonology, 2009, v. 44, n. 4, p. 402, doi. 10.1002/ppul.21028
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- Publication type:
- Article
Duration of treatment effect after tobramycin solution for inhalation in young children with cystic fibrosis.
- Published in:
- Pediatric Pulmonology, 2007, v. 42, n. 7, p. 610, doi. 10.1002/ppul.20625
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- Article
Author's response.
- Published in:
- Pediatric Pulmonology, 2003, v. 36, n. 5, p. 454, doi. 10.1002/ppul.10373
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- Publication type:
- Article
Risk factors for initial acquisition of Pseudomonas aeruginosa in children with cystic fibrosis identified by newborn screening.
- Published in:
- Pediatric Pulmonology, 2003, v. 35, n. 4, p. 257, doi. 10.1002/ppul.10230
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- Publication type:
- Article
Comparison of high-frequency chest wall oscillation and oscillating positive expiratory pressure in the home management of cystic fibrosis: A pilot study.
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- Pediatric Pulmonology, 2001, v. 32, n. 5, p. 372, doi. 10.1002/ppul.1146
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- Publication type:
- Article
Beclomethasone diproprionate reduced airway inflammation without adrenal suppression in young children with cystic fibrosis: A pilot study.
- Published in:
- Pediatric Pulmonology, 2001, v. 32, n. 4, p. 293, doi. 10.1002/ppul.1122
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- Publication type:
- Article
Safety of aerosolized INS 365 in patients with mild to moderate cystic fibrosis: Results of a phase I multi-center study.
- Published in:
- Pediatric Pulmonology, 2001, v. 32, n. 2, p. 122, doi. 10.1002/ppul.1098
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- Publication type:
- Article
Diagnostic accuracy of oropharyngeal cultures in infants and young children with cystic fibrosis.
- Published in:
- Pediatric Pulmonology, 1999, v. 28, n. 5, p. 321, doi. 10.1002/(SICI)1099-0496(199911)28:5<321::AID-PPUL3>3.0.CO;2-V
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- Publication type:
- Article
Infant lung function after inhaled nitric oxide therapy for persistent pulmonary hypertension of the newborn.
- Published in:
- Pediatric Pulmonology, 1999, v. 28, n. 1, p. 24, doi. 10.1002/(SICI)1099-0496(199907)28:1<24::AID-PPUL5>3.0.CO;2-M
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- Publication type:
- Article
Intestinal Lesions Are Associated with Altered Intestinal Microbiome and Are More Frequent in Children and Young Adults with Cystic Fibrosis and Cirrhosis.
- Published in:
- PLoS ONE, 2015, v. 10, n. 2, p. 1, doi. 10.1371/journal.pone.0116967
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- Publication type:
- Article
Evaluation of Circulating Proteins and Hemodynamics Towards Predicting Mortality in Children with Pulmonary Arterial Hypertension.
- Published in:
- PLoS ONE, 2013, v. 8, n. 11, p. 1, doi. 10.1371/journal.pone.0080235
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- Publication type:
- Article
Optimizing Nasal Potential Difference Analysis for CFTR Modulator Development: Assessment of Ivacaftor in CF Subjects with the <i>G551D-CFTR</i> Mutation.
- Published in:
- PLoS ONE, 2013, v. 8, n. 7, p. 1, doi. 10.1371/journal.pone.0066955
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- Publication type:
- Article
Inflammation and Airway Microbiota during Cystic Fibrosis Pulmonary Exacerbations.
- Published in:
- PLoS ONE, 2013, v. 8, n. 4, p. 1, doi. 10.1371/journal.pone.0062917
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- Publication type:
- Article
Reliability of Quantitative Real-Time PCR for Bacterial Detection in Cystic Fibrosis Airway Specimens.
- Published in:
- PLoS ONE, 2010, v. 5, n. 11, p. 1, doi. 10.1371/journal.pone.0015101
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- Publication type:
- Article
Temporal Response of the Fetal Pulmonary Circulation to Pharmacologic Vasodilators.
- Published in:
- Proceedings of the Society for Experimental Biology & Medicine, 1988, v. 187, n. 1, p. 89, doi. 10.3181/00379727-187-42642
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- Publication type:
- Article
Salt-Independent Abnormality of Antimicrobial Activity in Cystic Fibrosis Airway Surface Fluid.
- Published in:
- American Journal of Respiratory Cell & Molecular Biology, 2001, v. 25, n. 1, p. 21, doi. 10.1165/ajrcmb.25.1.4436
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- Publication type:
- Article
Azithromycin for Early Pseudomonas Infection in Cystic Fibrosis. The OPTIMIZE Randomized Trial.
- Published in:
- 2018
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- Publication type:
- journal article
Restoring Cystic Fibrosis Transmembrane Conductance Regulator Function Reduces Airway Bacteria and Inflammation in People with Cystic Fibrosis and Chronic Lung Infections.
- Published in:
- 2017
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- Publication type:
- journal article
Recovery of Acquired Cystic Fibrosis Transmembrane Conductance Regulator Dysfunction after Smoking Cessation.
- Published in:
- 2015
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- Publication type:
- Letter
Acquired defects in CFTR-dependent β-adrenergic sweat secretion in chronic obstructive pulmonary disease.
- Published in:
- Respiratory Research, 2014, v. 15, n. 2, p. 1, doi. 10.1186/1465-9921-15-25
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- Publication type:
- Article
Acquired defects in CFTR-dependent β-adrenergic sweat secretion in chronic obstructive pulmonary disease.
- Published in:
- 2014
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- Publication type:
- journal article
Parental attitudes toward newborn screening for cystic fibrosis.
- Published in:
- Pediatric Pulmonology, 1991, v. 11, n. S7, p. 23, doi. 10.1002/ppul.1950110706
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- Publication type:
- Article
Fat-soluble vitamins in infants identified by cystic fibrosis newborn screening.
- Published in:
- Pediatric Pulmonology, 1991, v. 11, n. S7, p. 52, doi. 10.1002/ppul.1950110711
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- Publication type:
- Article
Effect of Pancreatic Enzymes on Zinc Absorption in Cystic Fibrosis.
- Published in:
- Journal of Pediatric Gastroenterology & Nutrition, 1998, v. 26, n. 2, p. 136
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- Publication type:
- Article
Persistent morbidity and mortality of protein calorie malnutrition in young infants with CF.
- Published in:
- 1986
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- Publication type:
- journal article
Modifier gene study of meconium ileus in cystic fibrosis: statistical considerations and gene mapping results.
- Published in:
- Human Genetics, 2009, v. 126, n. 6, p. 763, doi. 10.1007/s00439-009-0724-8
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- Publication type:
- Article
Defective lipoxin-mediated anti-inflammatory activity in the cystic fibrosis airway.
- Published in:
- Nature Immunology, 2004, v. 5, n. 4, p. 388, doi. 10.1038/ni1056
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- Publication type:
- Article
Genome-wide association meta-analysis identifies five modifier loci of lung disease severity in cystic fibrosis.
- Published in:
- Nature Communications, 2015, v. 6, n. 9, p. 8382, doi. 10.1038/ncomms9382
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- Publication type:
- Article
Cystic fibrosis transmembrane conductance regulator and pseudomonas.
- Published in:
- 2014
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- Publication type:
- Editorial
Cystic Fibrosis Transmembrane Conductance Regulator and Pseudomonas.
- Published in:
- American Journal of Respiratory & Critical Care Medicine, 2014, v. 189, n. 7, p. 763, doi. 10.1164/rccm.201402-0209ed
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- Publication type:
- Article
Cigarette Smoke Induces Systemic Defects in Cystic Fibrosis Transmembrane Conductance Regulator Function.
- Published in:
- American Journal of Respiratory & Critical Care Medicine, 2013, v. 188, n. 11, p. 1321, doi. 10.1164/rccm.201304-0733OC
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- Publication type:
- Article
Future directions in early cystic fibrosis lung disease research: an NHLBI workshop report.
- Published in:
- 2012
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- Publication type:
- journal article
Future Directions in Early Cystic Fibrosis Lung Disease Research.
- Published in:
- American Journal of Respiratory & Critical Care Medicine, 2012, v. 185, n. 8, p. 887, doi. 10.1164/rccm.201111-2068WS
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- Publication type:
- Article
Circulating RNA transcripts identify therapeutic response in cystic fibrosis lung disease.
- Published in:
- 2008
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- Publication type:
- journal article
Update in cystic fibrosis 2007.
- Published in:
- 2008
- By:
- Publication type:
- journal article
Update in cystic fibrosis 2006.
- Published in:
- 2007
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- Publication type:
- journal article
Association between Pulmonary Function and Sputum Biomarkers in Cystic Fibrosis.
- Published in:
- American Journal of Respiratory & Critical Care Medicine, 2007, v. 175, n. 8, p. 822, doi. 10.1164/rccm.200609-1354oc
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- Publication type:
- Article
Update in Cystic Fibrosis 2006.
- Published in:
- American Journal of Respiratory & Critical Care Medicine, 2007, v. 175, n. 8, p. 754, doi. 10.1164/rccm.200701-160UP
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- Publication type:
- Article
Update in Cystic Fibrosis 2005.
- Published in:
- American Journal of Respiratory & Critical Care Medicine, 2006, v. 173, n. 9, p. 944, doi. 10.1164/rccm.2601006
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- Publication type:
- Article