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- Title
Bullous Kaposiform Hemangioendothelioma Masquerading as Aplasia Cutis Congenita.
- Authors
Steen, Aaron J.; Shin, Joseph H.; Pace, Nicole C.; Edgar, Mark; Clay, Michael R.; Linos, Konstantinos; Barton, Dorothea T.; Mann, Julianne A.
- Abstract
We present the case of a male infant with violaceous bullae on the scalp that were initially thought to be bullous aplasia cutis but at 3 months of age were diagnosed as a kaposiform hemangioendothelioma. This diagnosis should be considered when evaluating newborns with bullous plaques on the scalp that do not heal in the first 2-3 weeks of life. Kaposiform hemangioendothelioma ( KHE) is a rare vascular tumor that typically presents as a violaceous to purpuric plaque at birth or early infancy. It may be associated with Kasabach-Merritt phenomenon ( KMP), a potentially life-threatening consumptive coagulopathy.
- Subjects
ANGIOSARCOMA; BLISTERS; INFANT diseases; KASABACH-Merritt syndrome; BLOOD coagulation disorders; PEDIATRIC dermatology
- Publication
Pediatric Dermatology, 2016, Vol 33, Issue 5, pe267
- ISSN
0736-8046
- Publication type
Article
- DOI
10.1111/pde.12890