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- Title
Spontaneous splenic rupture in a patient with.
- Authors
Arcagök, Baran Cengiz; Özdemir, Nihal; Tekin, Ayşe; Özcan, Rahşan; Eliçevik, Mehmet; Şenyüz, Osman Faruk; Çam, Halit; Celkan, Tiraje
- Abstract
Afibrinogenemia is a rare bleeding disorder which is observed with an incidence of 1:1 000 000. It is an autosomal recessive disease and occurs as a result of mutation in one of the three genes which code the three polypeptide chains of fibrinogen. Basic clinical findings include spontaneous bleeding, bleeding after minor trauma or due to surgery. Splenic rupture in afibrinogenemia has been reported only in 6 cases so far. In this article, we present a 15-year old congenital afibrinogenemia patient with spontaneous splenic rupture.
- Subjects
BLOOD coagulation disorders; HEMORRHAGE; GENETIC mutation; ORGAN rupture; SPLENIC rupture
- Publication
Türk Pediatri Arşivi, 2014, Vol 49, Issue 3, p247
- ISSN
1306-0015
- Publication type
Article
- DOI
10.5152/tpa.2014.1070