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- Title
Cu-sil dentures: A novel approach of Papillon-Lefèvre syndrome management.
- Authors
Tyagi, Shreya; Thomas, Abi; Balla, Vinod; Kundra, Ruchika; Thomas, Abi M
- Abstract
Papillon-Lefèvre syndrome (PLS) is a rare genetic disorder characterized by palmoplantar keratosis and premature loss of primary and permanent dentition. Its onset can be as early as 1-4 years of age. The genetic disorder is mutation in the cathepsin C gene. Hereby, we discuss the fabrication of Cu-sil dentures for the prosthetic rehabilitation of a 14-year-old girl with PLS. The case report describes the procedure and associated relevant information regarding the management protocols.
- Subjects
DENTURES; GENETIC disorders; PERMANENT dentition; SYNDROMES; INFORMATION resources management; PALMOPLANTAR keratoderma; PROTEOLYTIC enzymes; PAPILLON Lefevre syndrome
- Publication
Journal of the Indian Society of Pedodontics & Preventive Dentistry, 2019, Vol 37, Issue 3, p303
- ISSN
0970-4388
- Publication type
case study
- DOI
10.4103/JISPPD.JISPPD_256_18