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- Title
Congenital absence of the portal vein associated with focal nodular hyperplasia of the liver and cystic dysplasia of the kidney.
- Authors
Guariso, G.; Fiorio, S.; Altavilla, G.; Gamba, P. G.; Toffolutti, T.; Chiesura-Corona, M.; Tedeschi, U.; Zancan, L.
- Abstract
Congenital absence of portal vein is a rare malformation. To date, 16 cases have been reported--all in association with other anomalies, i.e. benign or malignant hepatic neoplasms in 6 cases and cardiac malformations in 12. This case report described a girl with congenital absence of portal vein, focal nodular hyperplasia of the liver and cystic kidney dysplasia. Angiography showed the splenic vein and superior mesenteric vein joining to form a common trunk that entered the inferior vena cava directly above the liver. A review of the other cases in the literature is provided and the clinical aspects of our patient are discussed.
- Subjects
HUMAN abnormalities; DYSPLASIA; ANGIOGRAPHY; PORTAL vein; PATIENTS
- Publication
European Journal of Pediatrics, 1998, Vol 157, Issue 4, p287
- ISSN
0340-6199
- Publication type
journal article
- DOI
10.1007/s004310050812