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- Title
Ligneous conjunctivitis in a Dandy-Walker syndrome: A rare case report.
- Authors
Srirampur, Arjun; Ramappa, Muralidhar; Chaurasia, Sunita; Vemuganti, Geeta
- Abstract
Ligneous conjunctivitis (LC) is a rare form of pseudomembranous conjunctivitis seen in children, perhaps due to plasminogen deficiency, which manifest as a chronic refractory pseudomembranous conjunctivitis. LC cases are incapable in maintaining their fibrinolytic activity due to plasminogen deficiency; consequently, transudates of plasma assume as a thick, gelatinous, woody membranes over the mucosal surfaces. This is a short case report on a child with a LC, who presented with recurrent pseudomembranous conjunctivitis in conjunction with progressive congenital hydrocephalus due to aqueductal stenosis (Dandy-Walker syndrome). This rare association was clinically confirmed and prompt corrective surgical measures were instituted.
- Subjects
DANDY-Walker syndrome; CONJUNCTIVITIS; PLASMINOGEN; HYDROCEPHALUS; STENOSIS; COMPUTED tomography; CONJUNCTIVA; SYMPTOMS
- Publication
Indian Journal of Ophthalmology, 2019, Vol 67, Issue 1, p143
- ISSN
0301-4738
- Publication type
case study
- DOI
10.4103/ijo.IJO_772_18