We found a match
Your institution may have access to this item. Find your institution then sign in to continue.
- Title
Malformación de Chiari tipo I en un paciente con síndrome de Poland.
- Authors
Alcalá-Cerra, G.; Sabogal-Barrios, R.; Niño-Hernández, L.M.; Gutiérrez-Paternina, J.J.; Moscote-Salazar, L.R.; Preciado-Mesa, y E.
- Abstract
Chiari malformation type I and Poland's syndrome are two rare diseases and their simultaneous presentation had not been previously described in the literature. We report the case of a 27 year old male with history of Poland's syndrome, who referred headache and motor impairment of the intrinsic muscles of the left hand. In a cervical spine MR a Chiari I malformation with syringomyelia from C1 to T2 was found, which was treated by foramen magnum decompression, dural plasty and removal of the posterior arch of the atlas. A discussion of the embryological mechanisms that might be involved in the coexistence of these two entities is presented, emphasizing the role of para-axial mesoderm.
- Subjects
POLAND syndrome (Disease); ARNOLD-Chiari deformity; SYRINGOMYELIA; HEADACHE; MOTOR ability; ATLANTO-occipital joint; CERVICAL vertebrae; MAGNETIC resonance imaging
- Publication
Neurocirugía, 2011, Vol 22, Issue 6, p583
- ISSN
1130-1473
- Publication type
Article
- DOI
10.4321/S1130-14732011000600014