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- Title
(40) Erythropoietic protoporphyria with hepatic involvement.
- Authors
Barker, J. N. W. N.; Cerio, R.; France, D.; MacDonald, D. M.
- Abstract
This article presents the case study of patients suffering from erythropoietic protoporphyria (EPP) with hepatic involvement. This patient initially presented in the summer of 1958, aged 18 months, with intermittent redness and swelling of the face and hands. A liver biopsy performed in 1978 was normal apart from minimal pigment deposition. The hepatic histopathological and ultrastructural features observed in this case are characteristic of EPP. Hepatic fibrosis can frequently be present in the absence of abnormal liver function tests and may herald the onset of cirrhosis.
- Subjects
PORPHYRA; ERYTHROPOIETIN; LIVER diseases; CLINICAL pathology; LIVER function tests; PATHOLOGICAL physiology; ULTRASTRUCTURE (Biology)
- Publication
British Journal of Dermatology, 1988, Vol 119, p94
- ISSN
0007-0963
- Publication type
Article
- DOI
10.1111/j.1365-2133.1988.tb05443.x