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- Title
Enfermedad de Hailey-Hailey: comunicación de un caso tratado con naltrexona.
- Authors
Elizabeth Cameras-Melchor, Sara; de la Luz Romero-Vázquez, Ivonne; Guevara-Hernández, Cindy; Arellano-Mendoza, María Ivonne; Mercadillo-Pérez, Patricia
- Abstract
BACKGROUND: Benign familial pemphigus is a rare benign genodermatosis caused by mutations in the ATP2C1 gene. It is characterized by affecting areas of folds, with presentation of outbreaks of vesicles and blisters. Its pathogenesis is unclear. The diagnosis is clinical; however, a histopathological study is performed to corroborate it. Currently there is no specific treatment, and it depends on the evolution of each individual; however, the first treatment is corticosteroids and topical antibiotics. CLINICAL CASE: A 15-year-old male patient with a maternal branch family history of bullous dermatosis, who presented plaques with multiple papular-like lesions, hyperpigmented, dark brown, pruritic in the armpits and groin. The histopathological study confirmed Hailey-Hailey disease, starting treatment with naltrexone with a favorable evolution. CONCLUSIONS: Hailey-Hailey disease is a little-known condition that affects the quality of life of patients, so it is important to know about this disease to make the correct diagnosis and avoid the prescription of inappropriate drugs that can delay diagnosis or aggravate dermatosis.
- Publication
Dermatología Revista Mexicana, 2021, Vol 65, Issue 5, p757
- ISSN
0185-4038
- Publication type
Article
- DOI
10.24245/dermatolrevmex.v65i5.6906