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- Title
Split cord malformation with dorsally located bony spur: Report of four cases and review of literature.
- Authors
Prasad, G. L.; Borkar, Sachin A.; Satyarthee, G. D.; Mahapatra, A. K.
- Abstract
Split cord malformations (SCM) with a dorsally located bony spur are a very rare entity. The authors report a series of four such cases. The literature is reviewed regarding the pathogenesis and management of this uncommon variant of SCM. The presenting features include - scoliosis with motor and autonomic dysfunction ( n = 1), scoliosis with cutaneous patch ( n = 1), hypertrichotic area ( n = 1), and motor deficits alone ( n = 1). The location of spur was thoracic and lumbar in two patients (50%) each. Low-lying conus was present in three patients. Long segment syrinx was present in one patient. With respect to the bony anomalies, two patients had a hypertrophied posterior arch (HPA) and one patient had a dysraphic spine. All patients underwent surgical excision of the spur with detethering, if a low-lying conus was present. Two patients developed transient worsening of the neurological status after surgery which recovered at the time of the last follow-up; in both these patients, there was a HPA and a low-lying conus. Surgical excision of the spur with detethering of filum, in cases of low-lying conus, is the treatment of choice. Risk of post-operative worsening of the neurological status is increased in cases in which there is concomitant presence of HPA.
- Subjects
SPINAL cord abnormalities; SPINAL cord surgery; HUMAN abnormalities; MAGNETIC resonance imaging; METAPLASTIC ossification; PERIPHERAL neuropathy; SCOLIOSIS; DIAGNOSIS
- Publication
Journal of Pediatric Neurosciences, 2012, Vol 7, Issue 3, p167
- ISSN
1817-1745
- Publication type
Article
- DOI
10.4103/1817-1745.106469