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- Title
Severe Rhabdomyolysis in Phacomatosis Pigmentovascularis Type IIb associated with Sturge-Weber Syndrome.
- Authors
Bongjin Lee; Hyung Joo Jeong; Yu Hyeon Choi; Chong Won Choi; June Dong Park
- Abstract
Phacomatosis pigmentovascularis (PPV) is a rare syndrome characterized by concurrent nevus flammeus (capillary malformation) and pigmentary nevus. According to current research, the major pathophysiologic mechanism in PPV is venous dysplasia with resultant compensatory collateral channels and venous hypertension. Arterial involvement is rare. We herein report our experience on renovascular hypertension, intermittent claudication, and severe rhabdomyolysis due to diffuse stenosis of multiple arteries in a patient with PPV type IIb associated with SWS.
- Publication
Korean Journal of Critical Care Medicine (2383-4870), 2015, Vol 30, Issue 4, p329
- ISSN
2383-4870
- Publication type
Case Study
- DOI
10.4266/kjccm.2015.30.4.329