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- Title
VEXAS syndrome (vacuoles, E1 enzyme, X-linked, autoinflammatory, somatic).
- Authors
Varadarajan, A; Verghese, R M; Tirlangi, P K; Dass, J; Soneja, M; Seth, T
- Abstract
His chest radiograph showed a right-sided pleural effusion which revealed lymphocyte rich, exudative effusion with high adenosine deaminase levels on analysis; however, microbiological evidence of tuberculosis was lacking. Learning points for clinicians VEXAS syndrome (vacuoles, E1 enzyme, X-linked, autoinflammatory, somatic) manifests as an adult-onset autoinflammatory syndrome often associated with MDS.
- Subjects
SYNDROMES; SOMATIC mutation; ENZYMES; HYDROPS fetalis; PLEURAL effusions
- Publication
QJM: An International Journal of Medicine, 2023, Vol 116, Issue 4, p313
- ISSN
1460-2725
- Publication type
Article
- DOI
10.1093/qjmed/hcac259