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- Title
A review of cutaneous mucinoses in children.
- Authors
Rongioletti, F.
- Abstract
Summary: Mucin is a jelly‐like substance largely made of hyaluronic acid that is a normal component of the skin, usually produced by fibroblasts. However, in disease conditions called mucinoses, mucin accumulates in the skin in large amounts, causing swollen lesions (affected patches of skin) as it holds water. Cutaneous mucinoses are a group of diseases in adults that are uncommon in children. They include systemic (whole body) conditions such as scleromyxedema, pretibial mucinosis or scleredema, or skin‐limited conditions such as reticular erythematous mucinosis, localized lichen myxedematosus or cutaneous focal mucinosis. Cutaneous mucinoses occurring in childhood are less well understood than mucinoses in adults, because of the rarity of the diseases in children. The diagnosis and management of cutaneous mucinoses in children is also a difficult task due to a lack of adequate scientific knowledge or evidence‐based recommendations. The aim of this review is to help dermatologists and pediatricians identify patients with cutaneous mucinoses in childhood and enable them to start appropriate treatment. An attempt to build the first classification of childhood cutaneous mucinoses is proposed, to better clarify the issue. This summary relates to the study: Primary paediatric cutaneous mucinoses Linked Article: Rongioletti Br J Dermatol 2020; 182:29–38
- Subjects
SCIENTIFIC knowledge; HYALURONIC acid; JUVENILE diseases; PEDIATRICIANS; DERMATOLOGISTS; MUCINOUS adenocarcinoma
- Publication
British Journal of Dermatology, 2020, Vol 182, Issue 1, pe24
- ISSN
0007-0963
- Publication type
Article
- DOI
10.1111/bjd.18655