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- Title
Zinner syndrome - a case study of a rare triad of abnormalities in an adolescent patient.
- Authors
NOCUŃ-WASILEWSKA, Karolina; ZWOLIŃSKA, Danuta; KILIŚ-PSTRUSIŃSKA, Katarzyna; SZEWCZYK, Paweł; POLAK-JONKISZ, Dorota
- Abstract
Zinner syndrome [ZS] is a rare congenital malformation because of maldevelopment of mesonephric bud. The characteristic triad of anomalies comprising of seminal vesicle cyst, ipsilateral renal agenesis and ejaculatory duct obstruction. First symptoms of the disease (nonspecific abdominal pain, recurrent dysuria, infertility) are connected with large seminal vesicle cyst, occur at the age of increased sexual activity and the diagnosis is usually established in 3rd or 4th decade of life. Purpose of the presentation: Demonstration of a case of 15-years old boy accidentally diagnosed with Zinner syndrome during diagnosis of renal failure. Material and methods: A description of a case of a patient with afunctional and dysplastic left kidney followed up from his birth and referred to the Pediatric Nephrology Hospital because of litho-cystic structures under the bladder in control abdominal ultrasound. Results: On admission, current state was good, the patient without ailments. Laboratory results without abnormalities, a presence of lithocystic structures in abdominal ultrasound in anatomical localization typical for seminal vesicle. In pelvic MR, cystic dilatation of a left seminal vesicle filled with thick fluid content. The patient was classified for urological observation. Conclusions: 1. A congenital defect of one of the kidneys' can coexist with an ipsilateral seminal vesicle cyst. 2. Systematic ultrasound checkup of patients with a congenital renal defect could bring to final diagnosis and, through appropriate urological supervision prevent complications of the disease.
- Subjects
URETHRA abnormalities; WOLFFIAN body; POTTER'S syndrome; SEMINAL vesicles diseases; PEDIATRIC nephrology; UROLOGY
- Publication
Review of Medicine / Przeglad Lekarski, 2019, Vol 76, Issue 5, p286
- ISSN
0033-2240
- Publication type
Case Study