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- Title
Anesthetic management of a patient with methylmalonic acidemia: a case report.
- Authors
Uemura, Yuta; Kakuta, Nami; Tanaka, Katsuya; Tsutsumi, Yasuo M.
- Abstract
Background: Methylmalonic acidemia (MMA) is a metabolic disorder of organic acids and is characterized by the accumulation of methylmalonic acids.Case presentation: The patient was a 19-year-old female diagnosed with severe MMA at 3 days of age, who was scheduled for renal replacement therapy. Preoperatively, there was no evidence of metabolic acidosis or electrolyte abnormalities. Glucose was administered preoperatively following a 6-h fast. Anesthesia was administered using thiamylal, remifentanil, rocuronium, and sevoflurane. After tracheal intubation, the patient underwent an ultrasound-guided bilateral rectus sheath block with ropivacaine. A drop in blood sugar level was treated with 5% glucose. Extubation was performed after intravenous administration of sugammadex.Conclusions: We report the anesthetic management of a patient with MMA using a combination of general anesthesia and rectus sheath block.
- Subjects
ANESTHETICS; METHYLMALONIC acid; METABOLIC disorder treatment; ELECTROLYTES; INTRAVENOUS anesthesia
- Publication
JA Clinical Reports, 2018, Vol 4, Issue 1, p1
- ISSN
2363-9024
- Publication type
Article
- DOI
10.1186/s40981-018-0209-7