We found a match
Your institution may have access to this item. Find your institution then sign in to continue.
- Title
Rings and ovoid heart: OCIR. A new cardiomyopathy? Family genetic findings and multimodality imaging analysis. A rare cardiac phenotype and review of the literature.
- Authors
Preciado-Anaya, Andres; Preciado-Gutierrez, Oscar Ulises; Balderrabano-Saucedo, Norma; Hu, Dan; Zarate-Ordoñez, Fabiola; Castro-Villacorta, Humberto; Lazcano-Bautista, Sonia; Olmos-Temois, Sergio Gabriel; Leyva Reyes, Nestor Rafael; Barajas-Martinez, Hector
- Abstract
The first electrocardiogram (EKG) showed inappropriate sinus tachycardia with heart rate (HR) of 132 X'; right axis deviation, dextrorotation, electric vertical position, and second-degree right bundle branch block (Figure 1A). (B) EKG with maximum heart rate, 180 per minute, during the stress Bruce protocol test; the premature ventricular depolarization has right bundle branch block morphology and upper axis and is originated probably at the tip or in the free wall of the right ventricle. At the end of the stress test, an isolated premature ventricular depolarization was present with right bundle branch block morphology and upper axis, born probably at the tip or in the free wall of the right ventricle (Figure 1B), which is also in contact with the chest wall (Figure 3A, B). Discussion The MYBPC3 anomaly reported here can be found in about 40% of hypertrophic cardiomyopathy (HCM), rarely in left ventricular noncompaction (LVNC) or dilated cardiomyopathy.
- Subjects
PHENOTYPES; IMAGE analysis; TAKOTSUBO cardiomyopathy; VENTRICULAR outflow obstruction; CARDIOMYOPATHIES
- Publication
Journal of Nuclear Cardiology, 2021, Vol 28, Issue 1, p359
- ISSN
1071-3581
- Publication type
journal article
- DOI
10.1007/s12350-019-01999-z