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- Title
Intracranial juvenile xanthogranuloma in an infant.
- Authors
Myeong, Ho-Sung; Koh, Eun Jung; Cheon, Jung-Eun; Park, Sung-Hye; Kim, Seung-Ki
- Abstract
Juvenile xanthogranuloma (JXG) is a type of non-Langerhans cell histiocytosis that most commonly manifests as a solitary cutaneous lesion of the head and neck in children. Intracranial JXG is extremely rare. Although it is widely known that JXG skin lesions gradually disappear over time without treatment, treatment guidelines for intracranial JXG have not been established. It is very difficult to predict whether an intracranial lesion is JXG with only a pre-operative imaging work-up without pathologic confirmation. We report a case of the youngest, a 3-month-old male infant with an intracranial extra-axial mass with rapid growth for 2 months. Additionally, we suggest characteristic MRI findings for intracranial extra-axial JXG of a low T2 signal and a kidney bean shape.
- Subjects
JUVENILE xanthogranuloma; INFANTS; LANGERHANS-cell histiocytosis; NON-langerhans-cell histiocytosis; KIDNEY bean; ERDHEIM-Chester disease
- Publication
Child's Nervous System, 2021, Vol 37, Issue 10, p3265
- ISSN
0256-7040
- Publication type
Case Study
- DOI
10.1007/s00381-021-05088-w