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- Title
Kartagener syndrome - case report.
- Authors
Zugravu, Adina; Harabagiu, Oana; Cosgarea, Marcel
- Abstract
Background. Kartagener syndrome is a rare congenital disease characterised by a clinical triad of symptoms: situs inversus, chronic rhinosinusitis and bronchiectasis. Although congenital ciliary defect is recognised as the main cause of this syndrome, it remains difficult to treat the associated airway infection. Case report. A 3-year-old male patient presented with nasal obstruction, seromucous rhinorrhea, left exophthalmia. He also had situs inversus. Electron microscopic evaluation of his nasal mucosa revealed ciliary defect and confirmed the diagnosis of Kartagener syndrome. He underwent adenoidectomy. After a month he presents reappearance of the nasal obstruction with mucopurulent rhinorrhea and left exophthalmia. ENT exam reveals bilateral nasal polyposis. We performed FESS with bilateral polypectomy followed by long-term postoperative debridement of the sinonasal cavity and medical therapy (nasal irrigation, mucoactive agents, steroids and antibiotics). This treatment reduced chronic rhinosinusitis and protected against subsequent airway infection in a 3-year follow-up. Conclusion. FESS is effective for relieving both chronic rhinosinusitis and airway infection of Kartagener syndrome in the long term.
- Subjects
CONGENITAL disorders; DYSKINESIAS; SINUSITIS in children
- Publication
ORL.ro, 2016, Vol 9, Issue 31, p64
- ISSN
2067-6530
- Publication type
Abstract