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- Title
Pemphigus vulgaris in a patient with primary hypogammaglobulinemia: A case report.
- Authors
Musabak, Uğur Hacı; Erdoğan, Tuba; Tunca, Mustafa
- Abstract
Pemphigus vulgaris (PV) is a rare autoimmune disorder characterized by blisters on the mucous membranes and skin. Autoimmunity is an important complication developing in predominantly antibody deficiencies, which is a subgroup of primary immunodeficiencies (PID). Herein, we present a patient with PV who had primary antibody deficiency and whose disease relapsed during the maintenance period of conventional immunosuppressive treatments but progressed to remission following high-dose intravenous immunoglobulin therapy. Thus, we aimed to create awareness for the study of primary immunodeficiencies in rare autoimmune bullous diseases.
- Subjects
PEMPHIGUS treatment; PHYSICAL diagnosis; AUTOANTIBODIES; PEMPHIGUS; IMMUNOGLOBULINS; IMMUNOSUPPRESSION; IMMUNOLOGICAL deficiency syndromes; TREATMENT effectiveness; AGAMMAGLOBULINEMIA; DISEASE remission; SYMPTOMS
- Publication
Turkderm - Turkish Archives of Dermatology & Venereology, 2022, Vol 56, Issue 2, p80
- ISSN
2717-6398
- Publication type
Article
- DOI
10.4274/turkderm.galenos.2022.81370