Describes the case of a 53-year-old woman with combined cutis verticis gyrata (CVG) and Darier's disease. Presence of scaly, crusted, pruritic lesions; Persistent papular eruption on the upper part of the patient's back; Presence of deep furrows and folds on the forehead and scalp; Improvement in condition after treatment with acitretin; Involution of scalp furrows after treatment.