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- Title
Congenital erythropoietic porphyria -- Oral manifestations and dental treatment in childhood: A case report.
- Authors
Fayle, Stephen A.; Pollard, Maxine A.
- Abstract
Congenital erythropoietic porphyria is a rare condition resulting from an inborn error in prophyrin metabolism. This deficiency leads to hemolytic anemia, photosensitivity, blistering of the skin, and deposition of real-brown pigments in the bones and teeth. The literature regarding the dental aspects of this disorder is briefly reviewed and the preventive, restorative, and esthetic dental management of a 4-year-old child with congenital erythropoietic porphyria is described.
- Subjects
ERYTHROPOIESIS; HEMATOPOIESIS; PORPHYRIA; PIGMENTATION disorders; PORPHYRINURIA; DENTISTRY
- Publication
Quintessence International, 1994, Vol 25, Issue 8, p551
- ISSN
0033-6572
- Publication type
Article