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- Title
Cardiac Tumor in Juvenile Onset Behçet’s Disease: Case Report and Review of the Literature.
- Authors
Adams, Elizabeth E.; Aluquin, Vincent P. R.; Bingham, C. April; Stone, James R.; Pauliks, Linda B.
- Abstract
Behçet’s disease is a chronic multisystemic inflammatory disorder characterized by orogenital ulcerations, uveitis, and occasional cardiac involvement. This report describes an atypical presentation of pediatric Behçet’s disease with pulmonary emboli and a cardiac mass. A 16-year-old boy with a 2-year history of oral ulcers presented with weight loss, fever, joint pain, and a large tumor adhering to the free wall of the heart’s right ventricle. Surgical biopsy demonstrated endomyocarditis with thrombus formation and led to the diagnosis. At the 2-year follow-up evaluation, intracardiac thrombus and pulmonic emboli had not recurred. Symptom control with immunosuppressive therapy was good.
- Subjects
BEHCET'S disease; BIOPSY; PULMONARY embolism; MOUTH ulcers; IMMUNOSUPPRESSIVE agents
- Publication
Pediatric Cardiology, 2010, Vol 31, Issue 2, p277
- ISSN
0172-0643
- Publication type
Article
- DOI
10.1007/s00246-009-9565-4