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- Title
Hydroa vacciniforme‐like lymphoproliferative disorder: A retrospective study on clinicopathological characteristics of 32 cases.
- Authors
Xu, Wenfeng; Tan, Jingyi; Cai, Chenyu; Lei, Lei; Cao, Xian; Zhou, Hongling; Xu, Man
- Abstract
The clinicopathological features of 32 patients (17 females and 15 males) with a median age of 8 years (range, 1.5–21 years) from Southwestern China diagnosed with hydroa vacciniforme‐like lymphoproliferative disorder (HVLPD) were reviewed. At presentation, 6 patients showed only skin lesions, while 26 patients showed both skin lesions and systemic symptoms, including fever, lymphadenopathy and hepatosplenomegaly. As the disease progressed, systemic symptoms occurred in all patients. Follow‐up data of 29 patients showed that 14 patients were still alive with disease with a median follow‐up time of 22 months (range 3.6–71 months), and 15 patients died within a median follow‐up of 6 months (range 0–60 months).
- Subjects
CHINA; LYMPHOPROLIFERATIVE disorders; CLINICAL pathology; RETROSPECTIVE studies; LYMPHADENITIS; EPSTEIN-Barr virus
- Publication
Pediatric Dermatology, 2022, Vol 39, Issue 3, p372
- ISSN
0736-8046
- Publication type
Article
- DOI
10.1111/pde.14938