We found a match
Your institution may have access to this item. Find your institution then sign in to continue.
- Title
Congenital esophageal stenosis associated with esophageal atresia/tracheoesophageal fistula: clinical and radiologic features.
- Authors
Hye Jin Yoo; Woo Sun Kim; Jung-Eun Cheon; So-Young Yoo; Park, Kwi-Won; Sung-Eun Jung; Su-Mi Shin; In-One Kim; Kyung Mo Yeon
- Abstract
Congenital esophageal stenosis (CES) can be associated with esophageal atresia/tracheoesophageal fistula (EA/TEF). Because there are a variety of degrees of obstruction and symptoms of CES, it is frequently difficult to make a pre- and post-operative diagnosis of the distal CES associated with EA/TEF. To evaluate the clinical and radiologic features of congenital esophageal stenosis associated with esophageal atresia/tracheoesophageal fistula. We retrospectively reviewed postoperative esophagograms and medical records of 187 children (107 boys, 80 girls) who had primary repair of EA/TEF from 1992 to 2009 at our institution. We evaluated the incidence of CES, clinical findings, radiologic features and management of CES in these children. CES was diagnosed in 22 of 187 EA/TEF children (12%); one child had double CES lesions, for a total of 23 lesions. Ten of those 22 children (45%) had presented with significant symptoms of esophageal obstruction. The diagnosis of CES was delayed in 10 children (45%) until 1–10 years of age. On esophagogram, CES ( n = 23) was located in the distal esophagus ( n = 20, 87%) or mid-esophagus ( n = 3, 13%). The degree of stenosis was severe ( n = 6, 26%), moderate ( n = 10, 43%), or mild ( n = 7, 30%). Eight children, including two with unsuccessful esophageal balloon dilatation of CES, were treated surgically. Histologic examination revealed tracheobronchial remnant ( n = 7) or fibromuscular hyperplasia ( n = 1). One child with surgically treated CES developed achalasia at the age of 3 years 9 months. Esophagography after EA/TEF repair should be performed with a high index of suspicion for the presence of distal CES, because the diagnosis and adequate management of CES can often be delayed.
- Subjects
ESOPHAGEAL stenosis; ESOPHAGEAL atresia; FISTULA; MEDICAL radiology; HUMAN abnormalities
- Publication
Pediatric Radiology, 2010, Vol 40, Issue 8, p1353
- ISSN
0301-0449
- Publication type
Article
- DOI
10.1007/s00247-010-1603-0