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- Title
Outer Retina Rupture from Subretinal Blood with Spontaneous Sealing and Visual Recovery in Frosted Branch Angiitis from Familial Mediterranean Fever: A Case Report.
- Authors
Vofo, Brice Nguedia; Amer, Radgonde
- Abstract
Familial Mediterranean fever (FMF) is a rare autoinflammatory disorder. Ocular involvement is rare. The full spectrum and response to treatment is poorly understood. An 18-year-old girl previously diagnosed with FMF presented with sudden loss of vision in the left eye (LE). Best-corrected visual acuity (BCVA) in the LE was finger counting at 1.5 meters. Angiitis with mild "frosting," hemi-central retinal vein occlusion (HCRVO), and acute outer retina rupture (ORR) were observed in the LE. Systemic steroids were initiated immediately. The ORR was sealed 2 weeks later while vision improved to 6/15 (near vision: J2) 5 months later. No recurrences were observed over 5 years of follow-up. We report a rare manifestation of frosted branch angiitis with concomitant HCRVO and ORR in a young patient with FMF. Closure of ORR was attained and vision recovered after treatment with high-dose steroids.
- Subjects
VASCULITIS treatment; STEROID drugs; RETINA; TREATMENT effectiveness; VISUAL acuity; RETINAL diseases; VISION disorders; AUTOINFLAMMATORY diseases; DISEASE complications
- Publication
Turkish Journal of Ophthalmology / Turk Oftalmoloji Dergisi, 2022, Vol 52, Issue 4, p286
- ISSN
1300-0659
- Publication type
Article
- DOI
10.4274/tjo.galenos.2022.69337