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- Title
A Rare Initial Presentation of Primary Diffuse Leptomeningeal PNET in a 10-Year-Old-Male.
- Authors
Paul Lim, Peter; Ramdas, Jagadeesh; Miller, Michal Ann; Schuerch, Conrad; Wu, George
- Abstract
Primary leptomeningeal primitive neuroectodermal tumors (PNETs) are extremely rare childhood central nervous system malignancies harboring a very poor prognosis. There is no consensus treatment for these tumors to date. We report a case of a 10-year-old male who presented with mental status change, hydrocephalus, intracranial and spinal diffuse leptomeningeal enhancement without a primary mass upon cranial imaging and a negative initial biopsy until five months into his presentation. He responded significantly well to initial chemotherapy and radiotherapy.
- Subjects
MENINGEAL cancer; NERVOUS system abnormalities; NEUROLOGICAL disorders; COMPUTED tomography; INTRACRANIAL pressure
- Publication
South Dakota Medicine, 2017, Vol 70, Issue 12, p543
- ISSN
0038-3317
- Publication type
Case Study