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- Title
PAPILLON-LEFÈVRE SYNDROME: AN UNUSUAL CASE REPORT.
- Authors
Özkan, Gökhan; Kanli, Aydan; Halici, Saniye Eren
- Abstract
Papillon-Lefèvre syndrome (PLS) is a rare autosomal disorder characterized by palmoplantar hyperkeratosis and periodontal problems leading to premature loss of both primary and permanent dentitions. It is caused by mutation of cathepsin C gene generating deficiency in host immune response to microorganisms. Up to date, no sexual or racial predominance has been detected. This paper report the diagnosis and rehabilitation procedures for a 14-year-old male patient with PLS.
- Subjects
PAPILLON Lefevre syndrome; PALMOPLANTAR keratoderma; TOOTH loss; CATHEPSINS; IMMUNE response
- Publication
International Journal of Dental Clinics, 2015, Vol 7, Issue 3, p28
- ISSN
2231-2285
- Publication type
Case Study