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- Title
Dorsal Enteric Sinus with Spina Bifida: A Rare Form of Split Notochord Syndrome.
- Authors
Nanda, Monika; Bawa, Monika; Kanojia, Ravi Prakash; Rao, K. L. N.
- Abstract
Split notochord syndrome is a rare congenital malformation that results in spinal anomalies associated with anomalies of the gastrointestinal tract and central nervous system. This report presents an infrequently described variant of this syndrome. A 9-month-old female presented with a dorsal midline mass since birth which was partially covered by skin, and part of the lesion gave a gross appearance of intestinal mucosa. MRI was suggestive of partial sacral agenesis with spinal dysraphism with tethered cord. Excision of the mass with repair of the spinal defect was done. Histopathology confirmed the presence of gastrointestinal mucosa. Copyright © 2010 S. Karger AG, Basel
- Subjects
CASE studies; SPINAL cord abnormalities; CENTRAL nervous system abnormalities; GASTROINTESTINAL system abnormalities; NEURAL tube defects; HUMAN abnormalities; GASTROINTESTINAL mucosa
- Publication
Pediatric Neurosurgery, 2010, Vol 46, Issue 2, p138
- ISSN
1016-2291
- Publication type
Article
- DOI
10.1159/000319398