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- Title
Kaposiform hemangioendothelioma of skull base with dura invasion in a pediatric patient: a case report.
- Authors
Jung, Seong-Chan; Jung, Tae-Young; Lee, Tae-Kyu; Kim, Yeong Jin; Baek, Hee Jo; Kim, Sung Soon
- Abstract
Kaposiform hemangioendothelioma is an extremely rare vascular tumor which shows aggressive local growth. We present a case of rapid growing vascular skull tumor with dura invasion in a pediatric patient with neurofibromatosis type 1. A 14-year-old male complained of headache and dizziness for 1 month after minor head trauma. Brain magnetic resonance imaging (MRI) revealed a 5-cm-sized tumor in the left frontotemporal bone with internal hemorrhage and cystic changes. The gross total resection of tumor was done. At the 7-month follow-up, brain MRI revealed a recurrent skull tumor with intracranial dura mass. He underwent second surgery, and the pathologic diagnosis was suggestive of Kaposiform hemangioendothelioma. For this vascular proliferative tumor, mTOR inhibitor was treated for 6 months, and there was the recurred nodular-enhancing mass along the sphenoid ridge. After additional 2 months of medication, the following MRI revealed a decreased nodular-enhancing mass.
- Subjects
CHILD patients; SKULL base; SKULL tumors; MAGNETIC resonance imaging; MTOR inhibitors; NEUROFIBROMATOSIS 1
- Publication
Child's Nervous System, 2023, Vol 39, Issue 11, p3289
- ISSN
0256-7040
- Publication type
Case Study
- DOI
10.1007/s00381-023-06025-9