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- Title
Multiple juvenile xanthogranulomata.
- Authors
García-Sirvent, Lucía; Espiñeira-Sicre, Joaquín; Ruiz-Sánchez, Juan; Cuesta-Montero, Laura
- Abstract
Juvenile xanthogranuloma is the most frequent form of non-Langerhans cell histiocytosis in children. Clinically, it presents as well defined, yellowish papules that are typically located on the head, neck, upper trunk, and proximal region of the extremities. Although solitary lesions are the most common presentation, few cases of multiple juvenile xanthogranuloma have been described, more frequently associated with extracutaneous involvement. We report a 2-month-old girl with 22 cutaneous papules, clinically and histologically compatible with juvenile xanthogranulomas. Screening of visceral involvement was performed with no evidence of systemic disease. Identifying high-risk factors of systemic disease in patients with multiple juvenile xanthogranuloma is essential to perform an appropriate management of this entity.
- Subjects
JUVENILE xanthogranuloma; NON-langerhans-cell histiocytosis; NEUROFIBROMATOSIS; TISSUE wounds; LEUKEMIA
- Publication
Dermatology Online Journal, 2024, Vol 30, Issue 1, p1
- ISSN
1087-2108
- Publication type
Article
- DOI
10.5070/D330163291