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- Title
Infantile Malignant Osteopetrosis: Report of 2 Cases With Osteomyelitis of the Jaws.
- Authors
Sekerci, Ahmet Ercan; Sisman, Yildiray; Ertas, Elif Tarim; Sahman, Halil; Aydinbelge, Mustafa
- Abstract
Infantile malignant osteopetrosis (IMO) is an uncommon autosomal recessive disease characterized by dense, brittle, sclerotic, radiopaque bones, which generally results in neurological and hematological abnormalities. In general, IMO is fatal, as patients fail to grow and expire due to complications of the disease such as severe chronic anemia, bleeding, and/or infections. In children with IMO, the development of the dentition is seriously disturbed. Patients with infantile osteopetrosis have a variety of signs and symptoms, including osteomyelitis of the jaws, which frequently and generally resists treatment. Infections may eventually become lethal; hence, jaw infection control is an important aspect of the disease for dentists and oral surgeons to consider. The purpose of this case report was to present 2 rare cases of pediatric patients (one of them died due to respiratory failure at 10 years old) diagnosed with osteopetrosis complicated by osteomyelitis of the jaw.
- Subjects
TURKEY; DENTAL radiography; MANDIBLE; MAXILLA; OSTEOMYELITIS; OSTEOPETROSIS; TOMOGRAPHY; BONE density; SOCIAL services case management; SYMPTOMS; DIAGNOSIS
- Publication
Journal of Dentistry for Children, 2012, Vol 79, Issue 2, p93
- ISSN
1551-8949
- Publication type
Article