We found a match
Your institution may have access to this item. Find your institution then sign in to continue.
- Title
Pulmonary Lymphangioleiomyomatosis: A Rare Case.
- Authors
AĞAÇKIRAN, Yetkin; ERTÜRK, Arzu; YEŞİLLER, Fatma İrem; HOCA, Nevin Taci; ÜSTÜN, Leyla Nesrin; ÇAPAN, Nermin
- Abstract
Lymphangioleiomyomatosis is an uncommon lung disease primarily affecting women of childbearing age. It is characterized by the progressive proliferation and infiltration of smooth muscle-like cells, which lead to cystic destruction of the lung parenchyma; obstruction of airways, blood vessels, and lymphatics; and loss of pulmonary function. We present the case of a 46-year-old female patient with chest pain, cough, sputum, and dyspnea on exertion for three weeks. Minimal pneumothorax was noted, and the patient was referred to our center for further investigation and treatment. High-resolution computed tomography revealed numerous bilateral thin-walled air cysts and interstitial thickening affecting the central and peripheral part of the upper zone of the lung. We performed an open-lung biopsy to confirm lymphangioleiomyomatosis. Our aim is to discuss the pathogenesis and other lesions noted in the differential diagnosis of this rare disease.
- Subjects
LYMPHANGIOMYOMATOSIS; DIFFERENTIAL diagnosis; LUNG disease treatment; LUNG tumors; IMMUNOHISTOCHEMISTRY; CELL proliferation; ARTERIAL occlusions; PNEUMOTHORAX; DIAGNOSIS
- Publication
Turkish Journal of Pathology, 2014, Vol 30, Issue 3, p233
- ISSN
1018-5615
- Publication type
Case Study
- DOI
10.5146/tjpath.2013.01190