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- Title
Glanzmann Thrombasthenia Associated with Siderotic Synovitis and Arthropathy: A Case Report.
- Authors
Alawad, Mouhammad J; Abu-Tineh, Mohammad; Alshurafa, Awni; Al-Taie, Alaa; Yousaf, Anil; Yassin, Mohamed A
- Abstract
Glanzmann thrombasthenia is a bleeding disorder with a low incidence. It typically manifests as superficial bleeding episodes, which tend to be mild. Deep organ involvement is not uncommon but remains rare due to the rarity of the disease itself and the unusual association between platelet disorders and deep organ implications. A 17-year-old boy with Glanzmann thrombasthenia since infancy developed ankle pain after a minor trauma. His initial workup was negative, but he continued to experience ankle pain. A magnetic resonance imaging (MRI) done after four weeks suggested siderotic synovitis. The patient was lost to follow-up after that and returned after two years with recurrent left ankle pain. Imaging and studies have shown evidence of chronic arthropathy. A specialized orthopedic team assessed the patient. The patient underwent intra-articular steroid injection for pain relief and was referred to continue physical therapy. In conclusion, hemarthrosis is more common in hemophilia than in platelet disorders and has potential morbidity and quality-of-life implications.
- Subjects
SYNOVITIS; JOINT diseases; MAGNETIC resonance imaging; ANKLE injuries; INTRA-articular injections; BLOOD platelet disorders; ANALGESIA
- Publication
Journal of Blood Medicine, 2023, Vol 14, p563
- ISSN
1179-2736
- Publication type
Case Study
- DOI
10.2147/JBM.S418937