We found a match
Your institution may have access to this item. Find your institution then sign in to continue.
- Title
Rare Congenital Dissecting Thoracic Aortic Aneurysm in a Child with Noonan Syndrome: A Case Report.
- Authors
Ahmad Maulana, Siti Aishah; Engku Alwi, Sharifah Huda; Hashim, Mohd Shafie; Abdul Rohim, Rabiatul Adawiyah
- Abstract
We present a rare case of congenital thoracic aortic aneurysm (TAA) complicated with dissection in a nine-year-old girl with Noonan syndrome and atrial septal defect. She presented with rapid breathing and upper respiratory tract symptoms. Chest X-ray revealed a huge upper mediastinum with cardiomegaly. Echocardiogram showed possible ascending TAA. Computerized tomography angiogram of the aorta revealed huge aortic root-ascending TAA with small aortic dissection. Despite immediate treatment, the patient passed away due to severe airway compromise.
- Subjects
DISSECTING aneurysms; RESPIRATORY diseases; THORACIC aneurysms; CHEST X rays; MEDIASTINUM; BLOOD vessels; CARDIAC hypertrophy; NOONAN syndrome; SURGICAL complications; ATRIAL septal defects; RISK assessment; ELECTROCARDIOGRAPHY; COMPUTED tomography; AORTIC dissection; RARE diseases; DISEASE risk factors
- Publication
Oman Medical Journal, 2023, Vol 38, Issue 6, p18
- ISSN
1999-768X
- Publication type
Article
- DOI
10.5001/omj.2023.66