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- Title
Renal Amyloidosis in a Common Variable Immune Deficiency Patient with Autoimmune Complications.
- Authors
AYTEKİN, Gökhan; ÇÖLKESEN, Fatih; YILDIZ, Eray; ESEN, Hacı Hasan; ARSLAN, Şevket
- Abstract
Common variable immune deficiency (CVID) is a rare primary immunodeficiency disorder that is characterized by defective antibody production and inadequate B cell differentiation. While frequently recurrent respiratory tract infections are the most prominent clinical feature in CVID patients, CVID is a heterogeneous immune deficiency disorder that involves many systems and organs such as lymphoid hyperplasia, autoimmune cytopenia, chronic lung diseases, granulomatous diseases and susceptibility to malignancy. This may lead to delay in diagnosis and immunoglobulin replacement therapy, not being able to receive antibiotics at the appropriate dose and time, chronic inflammation, and therefore secondary amyloidosis. In this case report it is aimed to present a CVID patient with autoimmune complications and developing renal amyloidosis during follow-up.
- Subjects
AMYLOIDOSIS diagnosis; THERAPEUTIC use of immunoglobulins; IMMUNOLOGICAL deficiency syndrome complications; AUTOIMMUNE diseases; COMMON variable immunodeficiency; KIDNEYS; DISEASE complications; SYMPTOMS
- Publication
Duzce Medical Journal, 2020, Vol 22, Issue 1, p67
- ISSN
1307-671X
- Publication type
Article
- DOI
10.18678/dtfd.693297