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- Title
Oral manifestations in Kindler syndrome: case report and discussion of literature findings.
- Authors
Barbosa, Nathalia Mocellin; Visioli, Fernanda; Martins, Manoela Domingues; Martins, Marco Antônio Trevizani; Munerato, Maria Cristina
- Abstract
Kindler syndrome is a rare genetic disorder showing some predominant clinical manifestations, for example, trauma-induced blisters, progressive poikiloderma, skin atrophy, and photosensitivity. Oral manifestations are not commonly described and can be often misdiagnosed. This report describes the case of a female patient diagnosed with Kindler syndrome showing the classical clinical features affecting the skin, in addition to oral lesions manifesting as keratotic plaques and ulcers affecting the buccal mucosa, floor of the mouth, alveolar ridge, hard palate, and soft palate. An incisional biopsy was performed to confirm the diagnostic hypothesis of an autoimmune lesion possibly related with the syndrome. Knowledge about the possible manifestations of the Kindler syndrome is important to improve its management.
- Subjects
SKIN diseases; ROTHMUND-Thomson syndrome; AUTOIMMUNE diseases; BIOPSY; BLISTERS; EPIDERMOLYSIS bullosa; ORAL diseases; PERIODONTAL disease; PHOTOSENSITIVITY disorders; SYSTEMATIC reviews; DISEASE complications
- Publication
Special Care in Dentistry, 2016, Vol 36, Issue 4, p223
- ISSN
0275-1879
- Publication type
journal article
- DOI
10.1111/scd.12165