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- Title
Life-threatening acute pneumonitis in mixed connective tissue disease: a case report and literature review.
- Authors
Rath, Eva; Zandieh, Shahin; Löckinger, Alexander; Hirschl, Mirko; Klaushofer, Klaus; Zwerina, Jochen
- Abstract
Mixed connective tissue disease (MCTD) is a rare connective tissue disease frequently involving the lungs. The main characteristic is a systemic sclerosis-like picture of slowly progressing interstitial lung disease consistent with lung fibrosis, while pulmonary arterial hypertension is rare. Herein, we present a case of a newly diagnosed MCTD patient developing life-threatening acute pneumonitis similar to lupus pneumonitis. Previous literature on this exceptionally rare complication of MCTD is reviewed and differential diagnosis and management discussed.
- Subjects
MIXED connective tissue disease; HYPERTENSION; PNEUMONIA; MULTIPLE sclerosis; DEMYELINATION
- Publication
Wiener Klinische Wochenschrift, 2015, Vol 127, Issue 19/20, p792
- ISSN
0043-5325
- Publication type
Article
- DOI
10.1007/s00508-015-0823-6