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- Title
The Extinction of Primary Polyarteritis Nodosa: A Modern Science Success Story?
- Authors
Kidder, Dana; Basu, Neil
- Abstract
The article provides insights into Polyarteritis Nodosa (PAN), a systemic necrotizing vasculitis affecting medium and small muscular arteries, characterized by aneurysm formation leading to organ ischemia. Over its storied history since 1866, PAN's classification has evolved, initially based on clinical phenotypes such as cutaneous-limited PAN (CPAN), later refined with the discovery of antineutrophil cytoplasmic antibodies (ANCAs) which differentiated it from microscopic polyangiitis.
- Subjects
INTERPROFESSIONAL relations; AGE distribution; HEPATITIS B; DISEASE relapse; NONSENSE mutation; KIDNEY diseases; POLYARTERITIS nodosa; PHENOTYPES; GASTROINTESTINAL diseases; DISEASE risk factors; DISEASE complications; SYMPTOMS
- Publication
Arthritis & Rheumatology, 2024, Vol 76, Issue 7, p996
- ISSN
2326-5191
- Publication type
Article
- DOI
10.1002/art.42851