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- Title
Acute intermittent porphyria presenting with neurological emergency: review of six cases.
- Authors
Kochar, Dhanpat K.; Pal, Mahender; Kochar, Sanjay Kumar; Vyas, Arvind; Kochar, Abhishek; Bindal, Dinesh; Agrawal, Rajender Prasad
- Abstract
Acute intermittent porphyria presenting with short duration of gastrointestinal symptoms followed by rapidly progressive fulminant neurological syndrome during first attack is relatively uncommon. It is a neurological emergency and mimics many other psychiatric and medical disorders and can be fatal if it remains undiagnosed and untreated. Further, specific treatment in the form of Heme arginate is not universally available and very costly, so high clinical suspicion and early diagnosis and management of acute attack and prevention of further attacks are very important. We report a series of six cases who presented with convulsion and/or polyneuropathy early in the course of disease to highlight this fact.
- Subjects
PORPHYRIA; NEUROLOGICAL emergencies; SEIZURES (Medicine); GASTROINTESTINAL system; POLYNEUROPATHIES; HEME
- Publication
Neurology India, 2007, Vol 55, Issue 4, p413
- ISSN
0028-3886
- Publication type
journal article
- DOI
10.4103/0028-3886.33303